Diagnostyka obrazowa choroby Coatsa

Background: Coats' disease is a rare congenital vascular abnormality of the retina consisting of multiple teleangiectases, breakdown of the retina-blood barrier, and formation of subretinal lipoproteinaceous exudate, leading to retinal detachment. Material/Methods: Globe imaging using US, CT, and MR was performed in five patients with decreased visual acuity (4 boys and 1 girl), aged 1-16 years, with a diagnosis or suspicion of Coats' disease. Results: Retinal thickening in the temporal quadrant was observed in one child. In the other four children, V-shaped retinal detachments with exudate accumulated beneath the detached retina were observed. All affected globes showed decreased anterior-posterior diameters compared with the contralateral eye. Calcifications of the retinal regions were not present. Conclusions: Globe imaging in Coats' disease precisely shows retinal abnormalities and typical subretinal exudates. These lesions are nonspecific and differentiation from other causes of exudative retinal detachment should be performed.